<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2183-1351</journal-id>
<journal-title><![CDATA[Acta Radiológica Portuguesa]]></journal-title>
<abbrev-journal-title><![CDATA[Acta Radiol Port]]></abbrev-journal-title>
<issn>2183-1351</issn>
<publisher>
<publisher-name><![CDATA[Sociedade Portuguesa de Radiologia e Medicina Nuclear]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2183-13512027000300901</article-id>
<article-id pub-id-type="doi">10.25748/arp.44910</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Imaging Features of Waldenström Macroglobulinemia: A Case Report]]></article-title>
<article-title xml:lang="pt"><![CDATA[Manifestações Imagiológicas da Macroglobulinemia de Waldenström: Relato de Caso]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Monteiro]]></surname>
<given-names><![CDATA[João R.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gomes]]></surname>
<given-names><![CDATA[Helena Martins]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Dias]]></surname>
<given-names><![CDATA[Marta Vaz]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Silva]]></surname>
<given-names><![CDATA[Beatriz Marques]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Albuquerque]]></surname>
<given-names><![CDATA[Chantal]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Almeida]]></surname>
<given-names><![CDATA[António]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,ULS de Viseu Dão-Lafões Serviço de Imagiologia ]]></institution>
<addr-line><![CDATA[Viseu ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>09</month>
<year>2027</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>09</month>
<year>2027</year>
</pub-date>
<volume>39</volume>
<numero>3</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.pt/scielo.php?script=sci_arttext&amp;pid=S2183-13512027000300901&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.pt/scielo.php?script=sci_abstract&amp;pid=S2183-13512027000300901&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.pt/scielo.php?script=sci_pdf&amp;pid=S2183-13512027000300901&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Waldenström macroglobulinemia is a rare subtype of non-Hodgkin lymphoma with bone marrow involvement and IgM overproduction. Patients may present with nonspecific symptoms or organ-related manifestations. Imaging, although not required for the diagnosis, can assess disease extent and monitor treatment. We report a 54-year-old male with weight loss, dyspnea, cervical lymphadenopathy and elevated IgM. CT revealed widespread lymphadenopathy, hepatosplenomegaly, renal infiltration and pulmonary consolidations. Bone marrow biopsy confirmed the diagnosis. Treatment with bendamustine and rituximab led to near-complete resolution on follow-up CT. This case highlights the diverse imaging features of Waldenström macroglobulinemia, including rare renal and pulmonary involvement and demonstrates the role of CT in disease evaluation and response monitoring.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo A macroglobulinemia de Waldenström é um subtipo raro de linfoma não-Hodgkin caracterizado pelo envolvimento da medula óssea e pela produção excessiva de IgM. Os doentes podem apresentar sintomas inespecíficos ou manifestações relacionadas com os órgãos afetados. Os exames de imagem, embora não sejam necessários para o diagnóstico, permitem avaliar a extensão da doença e monitorizar o tratamento. Relatamos o caso de um homem de 54 anos com perda de peso, dispneia, adenomegalias cervicais e níveis elevados de IgM. A TC revelou adenomegalias generalizadas, hepatoesplenomegalia, infiltração renal e consolidações pulmonares. A biópsia da medula óssea confirmou o diagnóstico. O tratamento com bendamustina e rituximab conduziu à resolução quase completa das alterações na TC de seguimento. Este caso evidencia a diversidade das manifestações imagiológicas da macroglobulinemia de Waldenström, incluindo o raro envolvimento renal e pulmonar e realça o papel da TC na avaliação da doença e no seguimento da resposta terapêutica.]]></p></abstract>
<kwd-group>
<kwd lng="pt"><![CDATA[Macroglobulinemia de Waldenstrom]]></kwd>
<kwd lng="pt"><![CDATA[Linfadenopatia]]></kwd>
<kwd lng="pt"><![CDATA[Tomografia computorizada]]></kwd>
<kwd lng="pt"><![CDATA[Doenças hematológicas]]></kwd>
<kwd lng="pt"><![CDATA[Doenças raras]]></kwd>
<kwd lng="pt"><![CDATA[Relatos de caso.]]></kwd>
<kwd lng="en"><![CDATA[Waldenstrom macroglobulinemia]]></kwd>
<kwd lng="en"><![CDATA[Lymphadenopathy]]></kwd>
<kwd lng="en"><![CDATA[Computed tomography]]></kwd>
<kwd lng="en"><![CDATA[Hematologic diseases]]></kwd>
<kwd lng="en"><![CDATA[Rare diseases]]></kwd>
<kwd lng="en"><![CDATA[Case reports.]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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</article>
