<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0872-0754</journal-id>
<journal-title><![CDATA[Nascer e Crescer]]></journal-title>
<abbrev-journal-title><![CDATA[Nascer e Crescer]]></abbrev-journal-title>
<issn>0872-0754</issn>
<publisher>
<publisher-name><![CDATA[Centro Hospitalar do Porto]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0872-07542022000400364</article-id>
<article-id pub-id-type="doi">10.25753/birthgrowthmj.v31.i4.27109</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Neonatal lupus erythematosus: A narrative review]]></article-title>
<article-title xml:lang="pt"><![CDATA[Lupus eritematoso neonatal: Uma revisão narrativa]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Marques]]></surname>
<given-names><![CDATA[Ana Raquel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rocha]]></surname>
<given-names><![CDATA[Gustavo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Soares]]></surname>
<given-names><![CDATA[Paulo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodrigues]]></surname>
<given-names><![CDATA[Mariana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pimenta]]></surname>
<given-names><![CDATA[Joana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Hospitalar Universitário de São João Department of Pediatric Cardiology ]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Centro Hospitalar Universitário de São João Department of Neonatology ]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Centro Hospitalar Universitário de São João Pediatric and Young Adult Rheumatology Unit ]]></institution>
<addr-line><![CDATA[Porto ]]></addr-line>
<country>Portugal</country>
</aff>
<pub-date pub-type="pub">
<day>30</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>30</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>31</volume>
<numero>4</numero>
<fpage>364</fpage>
<lpage>376</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.pt/scielo.php?script=sci_arttext&amp;pid=S0872-07542022000400364&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.pt/scielo.php?script=sci_abstract&amp;pid=S0872-07542022000400364&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.pt/scielo.php?script=sci_pdf&amp;pid=S0872-07542022000400364&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Introduction:  Neonatal lupus erythematosus (NLE) is characterized by the transplacental passage of maternal antibodies, mainly anti-Sjogren&#8217;s syndrome A/Ro (anti-SSA/Ro) and anti-Sjogren&#8217;s syndrome B/La (anti-SSB/La), which bind to the developing fetal tissues. Seropositive mothers may have a diagnosed disease, such as Sjögren&#8217;s syndrome, systemic lupus erythematosus, or undifferentiated connective tissue disease, but in 25&#9472;60% of cases, they are asymptomatic at the time of childbirth.  Objectives:  This article aimed to provide a narrative review of the current state of knowledge on NLE.  Development:  The clinical spectrum of NLE includes both reversible and irreversible features. Reversible clinical features, like cutaneous lesions, hematological and pulmonary abnormalities, and hepatobiliary dysfunction, disappear spontaneously as autoantibody levels decrease in the bloodstream. The most commonly reported NLE manifestation is cardiac disease. Injury to the cardiac conduction tissue may lead to defects, such as congenital atrioventricular (AV) block, which is the most severe and, in some cases, lethal NLE manifestation. NLE may also have an impact on the myocardium and endocardium, with maternal antibodies being responsible for endocardial fibroelastosis. Immune-mediated AV block may benefit from in-utero treatment with steroids. Hydroxychloroquine may also be prescribed to women with immune-mediated disorders in the preconception period.  Conclusions:  The management of infants affected with NLE should be performed in a tertiary care center. Postnatal pacemaker insertion may be indicated in the presence of irreversible AV block or heart failure. Erythrocyte or platelet transfusions, corticosteroids, or intravenous immunoglobulin may be indicated to treat severe disease manifestations.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo  Introdução:  O lúpus eritematoso neonatal caracteriza-se pela passagem transplacentária de anticorpos maternos, maioritariamente anti-síndrome de Sjögren A/Ro (anti-SSA/Ro) e anti-síndrome de Sjögren B/La (anti-SSB/La), que se ligam aos tecidos fetais em desenvolvimento. Mães seropositivas podem ter doença diagnosticada, nomeadamente síndrome de Sjögren, lúpus eritematoso sistémico, ou doença indiferenciada do tecido conjuntivo, mas em 25&#9472;60% dos casos são assintomáticas à data do parto.  Objetivos:  O objetivo deste estudo foi fazer uma revisão narrativa sobre o estado da arte do lúpus eritematoso neonatal.  Desenvolvimento:  As características clínicas do lúpus neonatal podem ser reversíveis ou irreversíveis. As características reversíveis, como lesões cutâneas, alterações hematológicas ou pulmonares e disfunção hepatobiliar, desaparecem espontaneamente à medida que os níveis de anticorpos circulantes diminuem, geralmente nos primeiros 6 a 8 meses de vida. A manifestação mais frequente de lúpus neonatal é doença cardíaca. A lesão do tecido de condução cardíaco pode resultar em bloqueio atrioventricular (AV) congénito, que constitui a manifestação mais grave e em alguns casos fatal de lúpus neonatal. A doença pode também ter impacto no miocárdio e endocárdio, dado que os anticorpos maternos podem causar fibroelastose endocárdica. O bloqueio AV imunomediado pode beneficiar do tratamento in utero com corticoides. Mulheres com patologia imunomediada podem também receber hidroxicloroquina no período pré-concecional.  Conclusões:  A abordagem de recém-nascidos com lúpus neonatal deve ser feita num centro terciário. Em presença de bloqueio AV irreversível ou sinais de insuficiência cardíaca, pode ser necessária a colocação de pacemaker após o nascimento. As manifestações graves da doença podem necessitar de transfusões de eritrócitos ou plaquetas, corticosteroides ou imunoglobulina endovenosa.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[antibody]]></kwd>
<kwd lng="en"><![CDATA[congenital atrioventricular block]]></kwd>
<kwd lng="en"><![CDATA[corticosteroid]]></kwd>
<kwd lng="en"><![CDATA[neonatal lupus erythematosus]]></kwd>
<kwd lng="en"><![CDATA[pacemaker]]></kwd>
<kwd lng="pt"><![CDATA[anticorpo]]></kwd>
<kwd lng="pt"><![CDATA[bloqueio auriculoventricular congénito]]></kwd>
<kwd lng="pt"><![CDATA[corticosteroide]]></kwd>
<kwd lng="pt"><![CDATA[lúpus eritematoso neonatal]]></kwd>
<kwd lng="pt"><![CDATA[pacemaker]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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